FENS  

FENS Forum 2008 - Geneva

- For posters, morning sessions: 9:30-13:30; afternoon sessions 13:30- 17:30.
  Authors are expected to be in attendance at their posters at the time indicated.
- For other sessions, time indicates the beginning and end of the sessions.
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Poster presentation 3 - Session 082 - Monday 14/07/2008, 09:30-13:30
Hall 1
C: Triplet repeat and ataxias

082.1. Poster board C1 - Mon 14/07/2008, 12:15 - Hall 1
Bailey J. (1), O'Connor V. (1), Chad J. (1), Biggs T. (2) & Perry H. (1)
(1) Southampton University, Southampton, England; (2) Capsant Neurotechnologies, Southampton, England
- CHARACTERISING THE THREE DIMENSIONAL POSTNATAL CORTICAL NEURONAL HI-SPOT SYSTEM.

082.2. Poster board C2 - Mon 14/07/2008, 11:30 - Hall 1
Bailly Y. (1), Haeberlé A. M. (1), Demais V. (2), Grant N. (1), Bombarde G. (1) & Heitz S. (1)
(1) INCI UMR7168 CNRS & Univ Louis Pasteur, Strasbourg, France; (2) IFR 37 Neurosciences de Strasbourg, Strasbourg, France
- AUTOPHAGIC CELL DEATH OF PURKINJE CELLS IN DOPPEL-EXPRESSING PRION PROTEIN-DEFICIENT MICE.

082.3. Poster board C3 - Mon 14/07/2008, 12:15 - Hall 1
Becker L. (1, 2), Kling E. (1, 2), Gailus-Durner V. (1), Fuchs H. (1), Hrabe De Angelis M. (1) & Klopstock T. (2)
(1) Inst. Exp. Genetics, Helmholtz Zentrum, Munich, Germany; (2) Dept. of Neurol., Friedrich-Baur-Inst., Munich, Germany
- NEUROLOGICAL PHENOTYPING OF MUTANT MOUSE MODELS IN THE GERMAN MOUSE CLINIC (GMC).

082.4. Poster board C4 - Mon 14/07/2008, 11:30 - Hall 1
Brindley R. L. & Weiss J. L.
Department of Biomedical Science, University of Sheffield, Sheffield, United Kingdom
- G-PROTEIN COUPLED RECEPTOR REGULATION OF P/Q-TYPE CALCIUM CHANNELS IN ATAXIA.

082.5. Poster board C5 - Mon 14/07/2008, 12:15 - Hall 1
Cendelin J., Voller J. & Vozeh F.
Dept. of Pathol. Physiol., Med. Fac., Charles Univ., Pilsen, Czech Republic
- QUANTIFICATION OF GAIT PARAMETERS IN ANIMAL MODEL OF CEREBELLAR ATAXIA.

082.6. Poster board C6 - Mon 14/07/2008, 11:30 - Hall 1
Cheung M. J. (1, 2), Gibbons H. M. (1), Dragunow M. (1) & Faull R. L. M. (2)
(1) Dept of Pharmacol & Clin Pharmacol. Uni of Auckland, Auckland, New Zealand; (2) Dept of Anat with Radiol. Uni of Auckland, Auckland, New Zealand
- A HUMAN BRAIN-DERIVED CELL CULTURE MODEL OF HUNTINGTONS DISEASE.

082.7. Poster board C7 - Mon 14/07/2008, 12:15 - Hall 1
Chintawar S. (1), Hourez R. (2), Ravella A. (1), Gall D. (2), Schiffmann S. N. (2) & Pandolfo M. (1)
(1) Lab. Exp. Neurol., Brussels, Belgium; (2) Lab. Neurophy., Brussels, Belgium
- GRAFTING NEURAL PRECURSOR CELLS IN SCA1 MOUSE MODEL.

082.8. Poster board C8 - Mon 14/07/2008, 11:30 - Hall 1
Choi Y. H., Park D. Y., Kim S., Kang T. H. & Kim K. T.
POSTECH, Pohang, Korea
- ACCUMULATION OF POLYGLUTAMINE AGGREGATES BY VACCINIA-RELATED KINASE 2 (VRK2).

082.9. Poster board C9 - Mon 14/07/2008, 12:15 - Hall 1
Chort A. (1, 2, 3), Janer A. (1, 2, 3), Latouche M. (1, 2, 3), Daret A. (1, 2, 3), Martin E. (1, 2, 3), Stevanin G. (1, 2, 3), Brice A. (1, 2, 3) & Sittler A. (1, 2, 3)
(1) INSERM UMR 679: Neur. and Exp. Therapeutics, Paris, France; (2) Pitié-Salpêtrière Hospital, Paris, France; (3) University Pierre and Marie Curie, Paris, France; (4) Dept. of Gen., Cytology and Embryology, Paris, France
- FIGHTING POLYGLUTAMINE DISORDERS BY BETA-INTERFERON TREATMENT: IN VITRO AND IN VIVO EVIDENCE.

082.10. Poster board C10 - Mon 14/07/2008, 11:30 - Hall 1
Ciamei A. & Morton A. J.
Dept. Pharmacol., Univ. Cambridge, Cambridge, United Kingdom
- INTERACTION BETWEEN STRIATAL AND HIPPOCAMPAL MEMORY SYSTEMS IS AGE-DEPENDENTLY UNBALANCED IN THE R6/2 MOUSE MODEL OF HUNTINGTON’S DISEASE.

082.11. Poster board C11 - Mon 14/07/2008, 12:15 - Hall 1
Corrochano-Sanchez S. (1), Acevedo Arozena A. (1), Rubinsztein D. C. (2) & Brown S. D. M. (1).
(1) MRC, Mammalian Genetics Unit, Harwell Oxfordshire, UK; (2) Addenbrooke's Hospital, Cambridge, UK
- IDENTIFYING GENES THAT MODIFY HUNTINGTON’S DISEASE IN THE MOUSE.

082.12. Poster board C12 - Mon 14/07/2008, 11:30 - Hall 1
Costa M. C. (1), Tomé R. J. (2), Macedo-Ribeiro S. (2), Logarinho E. (1) & Maciel P. (1)
(1) ICVS, School of Health Sciences, Univ of Minho, Braga, Portugal; (2) Inst for Mol and Cell Biology (IBMC), Porto, Portugal
- ATAXIN-3: A ROLE IN THE SCF COMPLEX?

082.13. Poster board C13 - Mon 14/07/2008, 12:15 - Hall 1
Costa V. (1, 2), Mormone E. (3, 4), Piacentini M. (4), Malorni W. (3) & Scorrano L. (1, 2)
(1) Dulbecco-Telethon Institute, VIMM, Padua, Italy; (2) Dept. of cell. physiology and Metabolism, CMU, Univ. of Geneva, Geneva, Switzerland; (3) Dept. of Drug Research and Evaluation, Ist. Superiore Sanità, Rome, Italy; (4) Dept. of Biology, Univ. of Rome "Tor Vergata", Rome, Italy
- EXPLORING THE ROLE OF THE OPA1-DEPENDENT CRISTAE REMODELLING PATHWAY IN THE MITOCHONDRIAL ALTERATIONS OF HUNTINGTON’S DISEASE.

082.14. Poster board C14 - Mon 14/07/2008, 11:30 - Hall 1
Durán R. (1, 2), Barrero F. (2, 3), Morales B. (2, 3), Quintela A. M. (1), Arce A. (1), Ramirez M. (4), Soler A. (1) & Vives Montero F. (1, 2)
(1) Dpt. Physiology, University of Granada, Granada, Spain; (2) Institute of Neurosciences, Granada, Spain; (3) Service of Neurology, Hospital clinico San Cecilio, Granada, Spain; (4) Dpt. of Health Sciences, University of Jaen, Jaen, Spain
- PLASMA AMINOPEPTIDASE ACTIVITY AND LIPID PEROXIDES IN HUNTINGTON DISEASE.

082.15. Poster board C15 - Mon 14/07/2008, 12:15 - Hall 1
Estrada Sánchez A. M. (1), Montiel T. (1), Segovia J. (2) & Massieu L. (1)
(1) Inst. Fisiol. Cel. Universidad Nacional Autónoma de México, Mexico City, Mexico; (2) CINVESTAV IPN, Mexico City, Mexico
- VULNERABILITY OF THE R6/2 HUNTINGTON’S DISEASE TRANSGENIC MICE TO GLUTAMATE-MEDIATED EXCITOTOXICITY DURING INHIBITION OF GLYCOLYTIC METABOLISM.

082.16. Poster board C16 - Mon 14/07/2008, 11:30 - Hall 1
Gambazzi L. (1), Gökce O. (2), Markram H. (1), Luthi-Carter R. (2) & Giugliano M. (1)
(1) Lab of Neural Microcircuitry, Brain Mind Institute, EPFL, Lausanne, Switzerland; (2) Functional Neurogenomics Lab, Brain Mind Institute, EPFL, Lausanne, Switzerland
- NETWORK-LEVEL ELECTROPHYSIOLOGICAL ABNORMALITIES IN A PRIMARY NEURONAL CULTURE MODEL OF HUNTINGTON’S DISEASE.

082.17. Poster board C17 - Mon 14/07/2008, 12:15 - Hall 1
Guncová I. (1), Mazurová Y. (1), Rudolf E. (2) & Látr I. (3)
(1) Dept. of Histol. and Embryol., Hradec Kralove, Czech Republic; (2) Dept. of Med. Biol. and Genet., Hradec Kralove, Czech Republic; (3) Neurosurgery Clinic, Hradec Kralove, Czech Republic
- THE COMPARISON OF PROGRESSION OF THE NEURODEGENERATIVE PROCESS IN HUNTINGTON’S DISEASED PATIENTS AND IN AN ANIMAL MODEL.

082.18. Poster board C18 - Mon 14/07/2008, 11:30 - Hall 1
Hannan A. J. (1, 2), Pang T. Y. (1, 2), Zajac M. (1, 2), Vijiaratnam N. (1), Barkus C. (1, 3), Clement O. (1), Howard M. (1) & Nithianantharajah J. (1)
(1) Howard Florey Inst., Univ. Melbourne, Melbourne, Australia; (2) Dept of Anat and Cell Biol., Univ. Melbourne, Melbourne, Australia; (3) Dept of Exp. Psychol., Univ. Oxford, Oxford, Australia
- GENE-ENVIRONMENT INTERACTIONS AND PATHOLOGICAL PLASTICITY IN THE R6/1 TRANSGENIC MOUSE MODEL OF HUNTINGTON'S DISEASE.

082.19. Poster board C19 - Mon 14/07/2008, 12:15 - Hall 1
Kandasamy M. (1), Rivera F. J. (1), Couillard-Despres S. (1), Raber K. (1, 2), Stephan M. (2), Winner B. (1), Olaf R. (2), Bogdahn U. (1), Winkler J. (1), Von Hoersten S. (2, 3) & Aigner L. (1)
(1) Dept of Neurol, Regensburg, Germany; (2) Dept of Appl Anatom, Hannover, Germany; (3) Exp Therapy, Erlangen-Nürnberg, Germany
- DELAYED NEURONAL DIFFERENTIATION AND IMPAIRED HIPPOCAMPAL NEUROGENESIS IN A TRANSGENIC RAT MODEL OF HUNTINGTON’S DISEASE.

082.20. Poster board C20 - Mon 14/07/2008, 11:30 - Hall 1
Lam J. (1), Imarisio S. (1, 2), Ttofi E. K. (2), Ueda R. (3), Rubinsztein D. C. (2) & O’Kane C. J. (1)
(1) Dept of Genetics, Univ of Cambridge, Cambridge, UK; (2) Cambridge Inst for Med Research, Cambridge, UK; (3) National Inst of Genetics, Mishima, Japan
- AN RNAI SCREEN FOR GENETIC MODIFIERS OF POLYGLUTAMINE DISEASES IN DROSOPHILA.

082.21. Poster board C21 - Mon 14/07/2008, 12:15 - Hall 1
Latouche M. (1), Drouet V. (1, 2), Martin E. (1), Chort A. (1), Michel P. P. (1), Duyckaerts C. (1), Janer A. (1), Sittler A. (1), Deglon N. (2), Barkats M. (3), Brice A. (1) & Stevanin G. (1)
(1) U679 Neurol. et Thérapeut. exp., Paris, France; (2) CEA Inst. of Biomed. Imaging & MIRCen, Orsay, France; (3) CNRS 91002 GENETHON FRE 3018, Evry, France
- SELECTIVE NEURONAL LOSS IN A CELL MODEL OF SPINOCEREBELLAR ATAXIA 7 REVEALS PATHOGENIC AND NORMAL FUNCTIONS OF THE ATAXIN 7 PROTEIN.

082.22. Poster board C22 - Mon 14/07/2008, 11:30 - Hall 1
Lee S. T., Chu K., Im W. S., Park J. E. & Kim M.
Neurodegeneration Res. Lab., Seoul Natl. Univ. Hosp., Seoul, South Korea
- INTRASTRIATAL TRANSPLANTATION OF HUMAN OLFACTORY NEUROEPITHELIAL CELLS ATTENUATES THE STRIATAL PATHOLOGY IN A TRANSGENIC MODEL OF HUNTINGTON’S DISEASE.

082.23. Poster board C23 - Mon 14/07/2008, 12:15 - Hall 1
Lim D. (1, 2), Fidrizzi L. (1, 2, 3), Tartari M. (4), Zuccato C. (4), Brini M. (2, 3) & Carafoli E. (1, 2)
(1) VIMM, Padua, Italy; (2) Dep. Biochem. Univ. Padova, Padua, Italy; (3) Dep. Exp. Vet. Sci. Univ. Padova, Padua, Italy; (4) Dep. Pharm. Sci. Univ. Milano, Milan, Italy
- CALCIUM AND MITOCHONDRIAL DYSFUNCTION IN HUNTINGTON'S DISEASE NEURONS.

082.24. Poster board C24 - Mon 14/07/2008, 11:30 - Hall 1
Martin E. (1), Latouche M. (1), Lasbleiz C. (2), Monnier V. (2), Debeir T. (1), Mouatt-Prigent A. (1), Muriel M. P. (1), Morel L. (1), Ruberg M. (1), Brice A. (1, 3), Tricoire H. (2) & Stevanin G. (1, 3)
(1) INSERM/UPMC UMR_S679, Paris, France; (2) Institut Jacques Monod, Paris, France; (3) APHP, Hôp. Pitié-Salpêtrière, Départ. Génèt. et Cytogénèt., Paris, France
- A CONDITIONAL PAN-NEURONAL DROSOPHILA MODEL OF SCA7 WITH ADULT REVERSIBLE PHENOTYPE RELIABLE FOR IDENTIFICATION OF MODIFIER GENES.

082.25. Poster board C25 - Mon 14/07/2008, 12:15 - Hall 1
Martínez-Laczano J. (1, 2), Rodríguez-Páez L. (2), Tenorio-López A. (3), Del Valle-Mondragon L. (3), Gonzalez-Esquivel D. (1), Pérez-Neri I. (1), Sánchez-Mendoza A. (3), Ríos C. (1) & Pérez-Severiano F. (1)
(1) Dept. de Neuroquímica INNyN, D. F., México; (2) Dept. de Bioquímica ENCB-IPN, D. F., México; (3) Dept. de Farmacología INC, D. F., México
- MODULATION OF THE KYNURENINE PATHWAY PROTECTS AGAINST NEURONAL DAMAGE IN A MODEL OF HUNTINGTON.

082.26. Poster board C26 - Mon 14/07/2008, 11:30 - Hall 1
Mezghrani A. (1), Monteil A. (1), Watschinger K. (2), Sinnegger-Brauns M. (2), Nargeot J. (1), Striessnig J. (2) & Lory P. (1)
(1) IGF, CNRS-UMR 5203, INSERM-U661, UM12, Montpellier, France; (2) Institut für Pharmazie und Centrum für Molekulare Biowissens, Innsbruck, Austria
- A DESTRUCTIVE INTERACTION MECHANISM ACCOUNTS FOR DOMINANT-NEGATIVE EFFECTS OF MISFOLDED MUTANTS OF VOLTAGE-GATED CA2+ CHANNELS.

082.27. Poster board C27 - Mon 14/07/2008, 12:15 - Hall 1
Morton A. J. (1), Sawiak S. J. (2), Wood N. I. (1), Williams G. B. (2) & Carpenter T. A. (2)
(1) Dept. Pharmacol., Univ. Cambridge, Cambridge, UK; (2) Wolfson Brain Imaging Centre, Univ. Cambridge, Cambridge, UK
- USE OF MAGNETIC RESONANCE IMAGING FOR ANATOMICAL PHENOTYPING OF THE R6/2 MOUSE MODEL OF HUNTINGTON’S DISEASE.

082.28. Poster board C28 - Mon 14/07/2008, 11:30 - Hall 1
Ortega Z. (1), Maynard C. (2), Díaz-Hernández M. (1), Hernández F. (1), Dantuma N. (2) & Lucas J. J. (1)
(1) Centro de Biol. Mol. "Severo Ochoa", Madrid, Spain; (2) Department of Cell and Mol Biol. (CMB), Karolinska In, Stockholm, Sweden
- ANALYSIS OF INDUCIBLE MOUSE MODEL OF HUNTINGTON'S DISEASE COMBINED WITH UBIQUITIN-PROTEASOME SYSTEM REPORTER MICE.

082.29. Poster board C29 - Mon 14/07/2008, 12:15 - Hall 1
Paganetti P., Weiss A., Klein C., Bibel M. & Regulier E.
NIBR / Neuroscience Discovery, Basel, Switzerland
- CELLULAR AND ANIMAL MODELS FOR HUNTINGTON’S DISEASE AND ANALYSIS OF PROTEIN AGGREGATES BY AGERA.

082.30. Poster board C30 - Mon 14/07/2008, 11:30 - Hall 1
Panaite P. A. (1), Gantelet E. (1), Kraftsik R. (2), Gourdon G. (3), Kuntzer T. (1) & Barakat-Walter I. (1, 2)
(1) Serv. Neurol. CHUV, UNIL, Lausanne, Switzerland; (2) Dept. Cell. Biol. and Morph. UNIL, Lausanne, Switzerland; (3) INSERM U383, Hosp. Necker, Paris, France
- MYOTONIC DYSTROPHY TRANSGENIC MICE EXHIBIT PATHOLOGICAL ABNORMALITIES IN THE DIAPHRAGM NEUROMUSCULAR JUNCTIONS AND PHRENIC NERVES.

082.31. Poster board C31 - Mon 14/07/2008, 12:15 - Hall 1
Paz-Villagran V., Jeantet Y. & Cho Y. H.
CNIC, Bordeaux, France
- CHANGES IN STRIATAL ACTIVITY DURING HABIT LEARNING IN R6/1 MICE.

082.32. Poster board C32 - Mon 14/07/2008, 11:30 - Hall 1
Pelegrí C. (1), Duran-Vilaregut J. (1), Del Valle J. (1), Pallàs M. (2), Camins T. (2) & Vilaplana J. (1)
(1) Dept. Fisiologia (Farmàcia), Universitat de Barcelona., Barcelona, Spain; (2) Unitat Farmacologia i Farmacognòsia (Farmàcia), UB., Barcelona, Spain
- CELL CYCLE ACTIVATION IN STRIATAL NEURONS FROM RATS TREATED WITH 3-NITROPROPIONIC ACID.

082.33. Poster board C33 - Mon 14/07/2008, 12:15 - Hall 1
Schiffmann S. N. (1), Millard I. (2), Servais L. (1, 3), Houtteman D. (1), Cuvelier L. (1), De Kerchove D'Exaerde A. (1), Cheron G. (3), Orr H. T. (4), Gall D. (1), Pandolfo M. (2) & Hourez R. (1)
(1) Lab. Neurophysiology, ULB, Brussels, Belgium; (2) Lab. Experimental Neurology, ULB, Brussels, Belgium; (3) Lab. Electrophysiology, UMH, Mons, Belgium; (4) Dept Neurology, Univ. Mississipi, Jackson, USA
- EARLY FUNCTIONAL ALTERATIONS IN PURKINJE CELLS CONTRIBUTE TO MOTOR IMPAIRMENT AND NEURODEGENERATION IN SPINOCEREBELLAR ATAXIA 1.

082.34. Poster board C34 - Mon 14/07/2008, 11:30 - Hall 1
Sinadinos C. A., Mudher A. K. & Wyttenbach A.
Neurosci. Grp. Biol., Southampton, Uk
- MODELLING HUNTINGTON’S DISEASE - ASSOCIATED AXONAL TRANSPORT DISRUPTION IN DROSOPHILA.

082.35. Poster board C35 - Mon 14/07/2008, 12:15 - Hall 1
Voller J., Cendelin J. & Vozeh F.
Dept. Pathol. Physiol., Med. Fac., Charles Univ., Pilsen, Czech Republic
- STRAIN DIFFERENCES IN GAIT IN B6CBA AND C3H WILD TYPE AND LURCHER MUTANT MICE.

082.36. Poster board C36 - Mon 14/07/2008, 11:30 - Hall 1
Wood N. I., Glynn D. & Morton A. J.
Dept. Pharmacol., Univ. Cambridge, Cambridge, UK
- COGNITIVE PRACTICE BUT NOT PHYSICAL TRAINING IMPROVES COGNITIVE PERFORMANCE IN A TRANSGENIC MOUSE MODEL OF HUNTINGTON’S DISEASE.

082.37. Poster board C37 - Mon 14/07/2008, 12:15 - Hall 1
Wyttenbach A., Hands S., Sajjad M. U. & Cuttle M.
University of Southampton, School of Biological Sciences, Southampton, United Kingdom
- DOES INTRACELLULAR PROTEIN MISFOLDING AND AGGREGATION CAUSE DYSREGULATION OF REDOX PROCESSES?


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